Endocardial fibroelastosis presenting with congenital complete heart block at birth

Fetal echocardiographic assessment of endocardial fibroelastosis in maternal anti-SSA antibody-associated complete heart block.

BACKGROUND There are few reports describing the features of maternal anti-SSA antibody-associated congenital complete heart block (CCHB) patients developing endocardial fibroelastosis (EFE). The aim of this study was to describe the clinical features and the outcome of patients with CCHB, with or without EFE. METHODS AND RESULTS Over a 20-year period, 12 consecutive patients diagnosed with ma...

CONGENITAL HEART DISEASE Cardiovascular magnetic resonance in endocardial fibroelastosis

Endomyocardial fibroelastosis (EFE) presents in a primary form that manifests in infancy as well as secondary forms related to hypereosinophilia and leukemic disorders (1). Accurate identification has previously required endomyocardial biopsy, though cardiovascular magnetic resonance (CMR) is uniquely suited to visualize endomyocardial fibrosis noninvasively. We present a case demonstrating CMR...

Congenital complete heart block.

Congenital Complete Heart Block.

Few of the reported cases of congenital complete heart block have been over twenty years of age. It seems, therefore, worth reporting seven cases who are in good health at various ages between 22 and 42 years. This aetiological factor should, therefore, be thought of in middle-aged and even in elderly patients with complete heart block of unknown oetiology. Campbell and Suzman (1934), reporting...

Congenital complete heart block.

seven hours twenty minutes before delivery, the foetal heart sounds became audible. The very slow rate was noted. It was regular, and the provisional diagnosis of complete heart block was suggested. At delivery the condition of the infant was good: there was no cyanosis. Auscultation of the heart disclosed no murmurs. The ventricular rate fluctuated from timne to timie and varied between sixty ...